62) Scharfe, C., Zaccaria, P., Hoertnagel, K., Jaksch, M., Klopstock, T., Lill, R., Prokisch, H., Gerbitz, K.D., Mewes, H.W., & Meitinger, T. MITOP: A database for mitochondria-related proteins, genes and diseases. (1999) Nucl. Acids Res. 27, 153-155.
63) Lange, H., Kispal, G., & Lill, R. (1999).
Reconstitution of iron transport to the site of heme synthesis
inside mitochondria. J. Biol. Chem. 274,
18989-18996.
64) Kispal, G., Csere, P., Prohl, C., & Lill, R. (1999).
The mitochondrial proteins Atm1p and Nfs1p are required for
biogenesis of cytosolic Fe/S proteins EMBO J. 18,
3981-3989.
65) Grad, L.I., Descheneau, A.T., Neupert, W., Lill, R., &
Nargang, F.E. (1999).
Inactivation of the Neurospora crassa mitochondrial outer
membrane protein TOM70 by repeat induced point mutation (RIP) causes
defects in mitochondrial protein import and morphology.
Curr. Genetics 36, 137-146.
66) Prohl, C., Kispal, G., & Lill, R. (1999).
Branched-chain amino acid transaminases from Saccharomyces
cerevisiae. Methods Enzymol., 324, 365-375.
67) Diekert, K., Kispal, G., Guiard, B. & Lill, R. (1999).
A novel targeting signal directing proteins into the
mitochondrial intermembrane space. Proc. Natl. Acad. Sci.
U.S.A. 96, 11752-11757.
68) Lill, R., Diekert, K., Kaut, A., Lange, H., Pelzer, W., Prohl, C.,
& Kispal, G. (1999).
The essential role of mitochondria in the biogenesis of
cellular iron-sulfur proteins. Biol. Chem. 380,
1157-1166.
69) Plesofsky, N., Gardner, N., Lill, R., & Brambl, R. (1999).
Disruption of the gene for Hsp30, an ?-crystallin-related heat
shock protein of Neurospora crassa, causes defects in import of
proteins into mitochondria. Biol. Chem. 380,
1231-1236.
70) Chinnery, P.F., Taylor, R.W., Diekert, K., Lill, R., Turnbull,
D.M., & Lightowlers, R.N. (1999).
Peptide Nucleic Acid delivery into human
mitochondria. Gene Therapy 6, 1919-1928.
71) Lange, H., Kaut, A., Kispal, G., & Lill, R. (2000).
A mitochondrial ferredoxin is essential for biogenesis of
intra- and extra-mitochondrial Fe/S proteins. Proc. Natl.
Acad. Sci. U.S.A. 97, 1050-1055.
72) Scharfe, C., Zaccaria, P., Hoertnagel, K., Jaksch, M., Klopstock,
T., Dembowski, M., Lill, R., Prokisch, H., Gerbitz, K.D., Neupert, W.,
Mewes, H.W., Meitinger, T.(2000).
MITOP, the mitochondrial proteome database: 2000
update. Nucleic Acids Res. 28, 155-158.
73) Rawls, J., Knecht, M., Diekert, K., Lill, R., & Löffler, M.
(2000).
Requirements for the mitochondrial import and localization of
dihydroorotate dehydrogenase. Eur. J. Biochem.
267, 2079-2087.
74) Lill, R. & Kispal, G. (2000).
Maturation of cellular Fe/S proteins: An essential function of
mitochondria. Trends Biochem. Sci. 25,
352-356.
75) Kaut, A., Lange, H., Diekert, K., Kispal, G., & Lill, R.
(2000).
Isa1p is a component of the mitochondrial machinery for
biogenesis of cellular Fe/S proteins and requires conserved cysteine
residues for function. J. Biol. Chem.
275, 15955-15961.
76) Mühlenhoff, U. & Lill, R. (2000).
Biogenesis of iron-sulfur proteins in eukaryotes: A novel task
of mitochondria that is inherited from bacteria. Biochem.
Biophys. Acta 1459, 370-382.
77) Bekri, S., Kispal, G., Lange, H., Fitzsimons, D., Lill,, R., &
Bishop, D.F. (2000).
The human ABC7 transporter: Gene structure and mutation in
X-linked sideroblastic anemia with ataxia (XLSA/A) causing disruption
of cytosolic iron-sulfur protein biogenesis. Blood
96, 3256-3264.
78) Pelzer, W., Mühlenhoff, U., Diekert, K., Siegmund, K., Kispal, G.,
& Lill, R. (2000).
Mitochondrial Isa2p plays a crucial role in the maturation of
cellular Fe/S proteins. FEBS Letters 476,
134-139.
